The main clinical manifestation of intestinal lymphangiectasia is a syndrome of malabsorption: diarrhea, vomiting, abdominal pain. In some cases, steatorrhea of varying severity occurs. Cystic cavity, deforming the villus. Hematoxylin and eosin stein.
Аннотация к работе
Severe form of primary intestinal limphangiectasia in one year old child Bulegenova M., Mustafin O., Makhneva A., Bekisheva A. Scientific center of pediatrics and children surgery, Almaty Summary: Primary intestinal lymphangiectasia (Waldman syndrome) is congenital abnormality of the lymphatic system in children - a disease that occurs infrequently. There are about 80 published descriptions of this pathology in infants. The main clinical manifestation of intestinal lymphangiectasia is a syndrome of malabsorption: diarrhea, nausea, vomiting, abdominal pain, peripheral edema. In some cases, steatorrhea of varying severity occurs. Long lasting of the disease, no effect on the therapy leads to such complications as chylous ascites and chylothorax. This article presents a clinical case of an early debut primary intestinal lymphangiectasia in 6-month-old child, complicated by development of concomitant immunodeficiency. The final diagnosis was set after the histological examination of biopsy material in jejunum. Su